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3 associated genes
7 signs/symptoms
COMMON GENES: 1
1 associated gene
No signs/symptoms info
Mantle cell lymphoma
Ataxia-telangiectasia variant

ATM ATM
CCND1
IGH


COMMON
GENES
ATM



Citations in the biomedical literature:


Mantle cell lymphoma
ATM CCND1 IGH
Ataxia-telangiectasia variant



Mantle cell lymphoma
Ataxia-telangiectasia variant

Synonym(s):
- LCM
- MCL
- Mantle zone lymphoma

Synonym(s):
- v-AT

Classification (Orphanet):
- Rare hematologic disease
- Rare oncologic disease
Classification (Orphanet):
- Rare genetic disease
- Rare neurologic disease

Classification (ICD10):
- Neoplasms -
Classification (ICD10):
- Diseases of the nervous system -

Epidemiological data:
Class of prevalence: 1-9 / 100 000
Average age onset: adulthood
Average age of death: adult
Type of inheritance: multigenic/multifactorial
Epidemiological data:
(no data available)

External references:
No OMIM references
1 MeSH reference: D020522
External references:
No OMIM references
No MeSH references

Mantle cell lymphoma

Very frequent
- Hematologic / blood / lymphatic cancer
- Lymphadenopathy / polyadenopathies

Frequent
- Anorexia
- Asthenia / fatigue / weakness
- Bone marrow / medullar infiltration
- Splenomegaly
- Weight loss / loss of appetite / break in weight curve / general health alteration



Ataxia-telangiectasia variant

(no data available)